KUALA LUMPUR, 17 April — World Haemophilia Day is observed each year on 17 April. This year’s theme is “Reaching out – connect to your community”.
The results of a real-world study “Bleeding and safety outcomes in persons with haemophilia A without inhibitors: Results from a prospective non‐interventional study in a real‐world setting” were announced recently in the journal Haemophilia.
It found that regular preventive treatment was able to at least partially prevent bleeding episodes in adolescent and adult males with severe hemophilia A and without inhibitors.
People with hemophilia A may experience bleeds even with prophylactic treatment with engineered factor VIII (FVIII), which is the missing or defective clotting protein.
Haemophilia is a rare disorder in which the blood does not clot properly. People with this condition bleed for longer than usual as they lack a clotting factor, which works with platelets to cease bleeding at the site of an injury. This condition is usually inherited and affects mostly men.
The severity varies from person to person and causes excessive bleeding and poor blood clotting. There is no cure for the condition.
Most people suffer in silence due to lack of awareness, understanding and invisibility of the disorder. People are also affected due to social stigma.
Excessive bleeding from cuts, injuries, pain joint swelling, nose bleeds are symptoms. Replacement therapy, demand therapy, prophylactic therapy, pain relievers, physiotherapy are medical options which can provide relief to affected people.
According to the World Federation of Haemophilia, about 1 in 10,000 people are born with the bleeding disorder.